Definición:
Congenital resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the . The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the and .
Sinónimos:
Megacolon Congénito /
Megacolon Congenito /
Aganglionosis Colónica /
Aganglionosis del Colon /