Définition:
A slowly progressive autosomal dominant disorder of keratinization characterized by pinkish-to-tan papules that coalesce to form plaques. These lesions become darker over time and commonly fuse, forming papillomatous and warty malodorous growths.
Synonyme(s):
Dyskératose de Darier /
Dyskératose folliculaire de Darier /
Maladie de Darier /