Definition:
Rare, autosomal recessive disorder occurring between the first and fifth years of life. It is characterized by palmoplantar keratoderma with periodontitis followed by the premature shedding of both deciduous and permanent teeth.
Synonym(s):
Papillon-Lefevre Syndrome /
Disease, Papillon-Lefevre /
Papillon Lefevre Disease /
Papillon Lefevre Syndrome /