Definition: Group of disorders characterized by monoclonal proliferation of CD1+ HISTIOCYTES. The demonstration of the LANGERHANS CELLS Birbeck granules is the gold standard of the phenotype. EOSINOPHILIC GRANULOMA makes up 60-80% of all the cases. Synonym(s): Histiocytosis X / Langerhans-Cell Granulomatosis / Hand-Schueller-Christian Syndrome / Histiocytosis, Generalized / Narrow term(s): Eosinophilic Granuloma
Broader term(s): - Lung Diseases - Lymphoma - Neoplasms
Subheadings: complications / diagnosis / embryology / epidemiology / etiology / metabolism / microbiology / surgery / therapy
Broader term(s): - Lung Diseases, Interstitial - Lung Diseases - Respiratory Tract Diseases - Histiocytosis - Lymphoma - Neoplasms
Broader term(s): - Lung Diseases