Definition:
Congenital resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the . The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the and .
Synonym(s):
Aganglionosis, Colonic /
Colonic Aganglionosis /
Megacolon, Congenital /
Aganglionosis, Rectosigmoid Colon /