Beschreibung:
Group of disorders characterized by monoclonal proliferation of CD1+ HISTIOCYTES. The demonstration of the LANGERHANS CELLS Birbeck granules is the gold standard of the phenotype. EOSINOPHILIC GRANULOMA makes up 60-80% of all the cases.
Synonym(s):
Histiozytose X /
Langerhanszell-Granulomatose /
Histiocytosis X /