Beschreibung:
An idiopathic syndrome characterized by one or more of the following; recurrent orofacial swelling, relapsing facial paralysis, and fissured tongue (lingua plicata). The onset is usually in childhood and relapses are common. Cheilitis granulomatosa is a monosymptomatic variant of this condition. (Dermatol Clin 1996 Apr;14(2):371-9; Magalini & Magalini, Dictionary of Medical Syndromes, 4th ed, p531)
Synonym(s):
Cheilitis granulomatosa mit Fazialisneuropathie und orofazialem Ödem /
Granulomatöse Cheilitis /
Cheilitis granulomatosa /