Beschreibung:
Congenital resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the . The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the and .
Synonym(s):
Megacolon congenitum /
Morbus Hirschsprung /
Aganglionose, Kolon- /
Kolonaganglionose /